A Case of ANCA-associated Large Vessel Vasculitis with Multiple Saccular Aneurysms.

Aortitis is rare, but can occur in antineutrophil cytoplasm autoantibody (ANCA)-associated vasculitis (AAV)1. A high titer of proteinase 3 (PR3)-ANCA and renal involvement also suggest AAV. Giant cell arteritis, Behcet disease, and IgG4-related disease may account for multiple saccular aneurysms2,3,4. A 66-year-old man presenting with persistent fever, …