A rare case of Eruptive Vellus Hair Cysts: facial variant

Eruptive vellus hair cysts are rare benign tumors of pilosebaceous unit with vellus hairs, which appear in childhood or young adults. Their etio-pathogenesis is poorly known. A review of the literature shows that eruptive vellus hair cysts (EVHC) might be inherited as autosomal dominant or acquired, and might be associated with other genodermatoses like pachyonychia congenita and anhidrotic ectodermal dysplasia. Although it is a benign tumor of pilosebaceous unit, this condition is rather difficult to treat. Here we report a case of 23 years old female with multiple, asymptomatic, slate-grey to bluish papules on face and ears for last 5 years, with a positive family history of similar lesions in other siblings. To the best of our knowledge, this is the first case of autosomal dominant facial variant of eruptive vellus hair cysts to be published from Pakistan.