Pediatric Primary splenic angiosarcoma: A very rare disease.

The primary splenic angiosarcoma is a rare and aggressive tumor. Diagnose primarily in adults over 40 years. There were less than ten pediatric cases reported. A 13-year-old presented to the emergency with left upper quadrant pain. Laboratory results revealed anemia (11.3 g / dL) with normal platelets (166. 109 / L). A heterogeneous formation with a major axis of 5 cm has been identified on the scan of the abdomen. Splenectomy by a laparotomy was performed, and angiosarcoma Primary splenic was discovered. Seven months later, a scanner control showed no progressive disease, in particular, no liver metastases. She is currently alive without signs of progression. The primary splenic angiosarcoma is almost universally fatal, despite treatment. The best chance of survival is early diagnosis and splenectomy before the breaking of the spleen.