EPIDEMIOLOGICAL ASPECTS OF CONGENITAL MALFORMATIONS OF THE BRONCHOPULMONARY SYSTEM IN CHILDREN OF THE AMUR REGION

Introduction. The important issues for pediatric pulmonological practice are considered to be congenital malformations of the bronchopulmonary system (CLM). However, the true place of CLM in the structure of all chronic lung diseases has not been determined so far. Aim. Analysis of the frequency and structure of CLM in children of the Amur Region. Materials and methods . The data of clinical observations for 287 patients for the period from 2000 to 2018 were taken. Inclusion criteria were nosological units related to Q32-34 paragraphs of The International Statistical Classification of Diseases and Related Health Problems (ICD-10). Patients groups were formed by complete method. Children with a diagnosis confirmed during the diagnostic program for these patients were considered as observation units.  Results . The quantity of children with congenital lung malformations is 30% of the children with chronic nonspecific lung diseases observed in the clinic. CLM were detected in 93% of the examined children. Major part of these malformations is associated with underdevelopment of bronchopulmonary structures (69.7%). Tracheal and bronchial CLM were detected in 5.6% of cases. Pulmonary vascular malformations were diagnosed in 1.4% of patients. 7 cases of congenital lung malformations were diagnosed antenatally (2.3%). 52 children required surgical treatment (18.1%). Conclusion . Due to the fact that CLM form the basis for the secondary formation of chronic inflammation, the study of its frequency and structure contributes to improving the quality of medical care for patients, which significantly improves the quality of life, reduces the incidence of exacerbations, disability and mortality rate from complications of CLM.