Imaging of Single Ventricle

Single ventricle is a unique entity with a complex anatomy and physiology where there is complete or partial absence of an interventricular septum. It is associated with high morbidity, mortality and resource usage. The palliation of this condition generally involves a univentricular repair which involves a creation of a complete cavopulmonary connection by incorporating the caval flow into the pulmonary circulation. The key to a successful procedure revolves around a preoperative comprehensive multimodality cardiac imaging. Multiple imaging techniques are used in a graded and complementary fashion in order to select the right patient for the Fontan procedure and to ensure good long-term outcomes. Echocardiography, cardiac MRI and cardiac CTA are the tools that are frequently used in the evaluation of this disease entity. Proper application of existing and novel techniques will hopefully make this complex evaluation simpler and ultimately lead to better outcomes.