Cor triatriatum and intracardiac anomalous pulmonary venous return: an inborn atrial flow inversion.

Abstract A neonate with diagnosis of non-obstructive intra-cardiac type total anomalous pulmonary venous connection presented with profound cyanosis in the first days of life. The pre-operative specialist echocardiographic examination also identified the presence of partial cor triatriatum dexter. The anatomical pattern of this exceedingly rare diseases association, its peculiar clinical presentation and the surgical management are herein discussed.