A CASE OF CONGENITAL MULTICYSTIC DYSPLASTIC KIDNEY COMBINED WITH RENAL HYPERTENSION

We report a case of congenital multicystic dysplastic kidney in a new born, in whom prenatal ultrasonography revealed multiple cysts in the right kidney, and an abdominal mass was palpated in the right upper quadrant. Exploration revealed multiple cysts in the right nonfunctioning kidney. The newborn had been diagnosed as congenital multicystic dysplastic kidney and followed up. At four months of age, hypertension and elevated plasma renin activity were noticed. After the newborn underwent nephrectomy, blood pressure and plasma renin activity were resolved. Microscopic inspection showed typical features of the congenital multicystic dysplastic kidney without malignant change. In Japan, 174 cases have been reported to June 1989. Generally, the treatment of the patient is surgical resection and postoperative complications are rare. We can find an opinion by Bloom et al, that non surgical approach is recommended because the disease has favorable prognosis. However, nephrectomy should be considered, since serious complications such as malignancy and hypertension have been associated in 1.7% of patients with retained congenital multicystic dysplastic kidney.