A Choledochal Cyst Resulting in Obstructive Jaundice in a Case with Gallbladder Agenesis: Report of a Case and Review of the Literature

Agenesis of the gallbladder (AGB) and choledochal cyst (CC) are among the rare conditions of congenital extrahepatic biliary tree anomalies. AGB results from the failure of the cystic bud to develop in the 4th week of intrauterine life. It normally develops from the caudal part of the hepatic diverticulum (1, 2). CCs are single or multiple dilatations of the intrahepatic or extrahepatic biliary tree. Here, we report choledochal cyst complications presenting as obstructive jaundice in a patient with gallbladder agenesis. This combination is very rare and a review of literature revealed only five such cases (3, 4).