[Wolfram's syndrome. Presentation of a case].

: The association of insulin-dependent diabetes mellitus (IDDM) and progressive optic atrophy, occasionally associated with other disorders, is known as Wolfram syndrome. Here is reported the case history of a 14 years old girl who presented IDDM, progressive optic atrophy, hearing loss, disturbed colour vision, hemeralopia and retarded sexual maturation.