Shunt and right ventricular structural findings in isolated anomalous pulmonary venous return in Turner syndrome

Background Isolated anomalous pulmonary venous return of one pulmonary vein is relatively rare (~1/1000) and has an unclear natural history. Patients with Turner syndrome (TS) have a relatively high incidence of partial anomalous pulmonary venous return (PAPVR). Our aim is to describe the natural history of unrepaired isolated anomalous pulmonary venous return and its hemodynamic consequences through analysis of cardiac volumetric data and Qp:Qs ratios in asymptomatic volunteers with TS.