Missing pearls: Mystery or myth –Case report

Tooth agenesis or failure in development of tooth is one of the most common congenital anomalies. Although absence of one or more teeth is common but absence of multiple teeth is rare. Oligodontia [OD] is one of the rarest genetic disorder or any developmental anomaly which represents the congenital agenesis of either six or more teeth in deciduous and their permanent successors or both dentitions excluding third molars. One of the etiology of congenital absence of teeth which is taken under consideration is rooted in heredity or developmental anomalies. Certain problems are encountered along with OD such as aesthetic, functional, and psychological problems, specifically if the anterior region is involved. OD can exhibit either as a solitary presentation or as a part of a syndrome. Here we present a case of OD in nine year old boy with a complaint of missing mandibular anterior teeth. Keywords: Mandibular, Deciduous, Oligodontia.