Enfermedad de coats recidivante diagnosticada en sujeto adulto

2007 
espanolCaso clinico: Paciente varon que con 30 anos tuvo el primer episodio de enfermedad de Coats y recurrencia 14 anos mas tarde. Clinicamente ambos episodios tienen como sintoma de inicio vision borrosa y exploracion tipica de exudacion masiva retiniana con corona de exudados duros. La angiografia presenta hallazgos caracteristicos de telangiectasia retiniana con dilatacion anormal de vasos con hiperfluorescencia precoz y fuga tardia. Discusion: Coats es una entidad clinica poco frecuente y con grado de severidad variable, que hacen dificiles los estudios randomizados prospectivos. Pese a los hallazgos caracteristicos, hay que descartar otros diagnosticos tanto en el nino como en el adulto causantes de esa misma clinica. EnglishCase report: A male diagnosed with Coats disease at the age of 30 years, had a relapse of this condition 14 years later. His first symptom of blurred vision occurred in both episodes and similar findings of unilateral retinal exudation and lipid deposition at boundary were seen. Angiography showed the characteristic early hyperfluorescence of the telangiectasias and late leakage of dye. Discussion: Coats disease is relatively uncommon and, as the degree of involvement varies from case to case, a randomized, prospective study of treatment would probably not be feasible. Despite the characteristic features of this disease, the differential diagnoses must be considered in both children and adults
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