An Unusual Discordant Atrioventricular Connection with Double Outlet Right Ventricle (DORV): A Clinical Experience with a 11-year-old Female Patient

Background: Atrioventricular discordant connection with DORV is a rare congenital cardiac anomaly and associated with various surgical procedures. We present a case of DORV in which the establishment of a three-dimensional (3D) printed model during perioperative period and the complex surgical procedure was performed. Case presentation: A 11-year-old girl, presented with a double outlet right ventricle (DORV). Her atrioventricular connection was discordant, her ventricular septal defect was far from the two major arteries but more relatively close to the aorta and an atrial switch (Senning operation) plus intraventricular tunnel repair connecting the left ventricle blood flow to aorta was successfully performed. Complete atrioventricular block was the only postoperative complication observed. Discussion and Conclusion: DORV in the setting of discordant atrioventricular connection is an extremely rare disease. Operation on a relatively older patient is scarce. In this case, we used 3D printed technique in this operation, but postoperative complete atrioventricular block occurred. It was hoped that we would have a longterm follow-up for this patient, providing more valuable clinical experience.