Challenges in the management of a rare atypical case of malignant glomus tumour of the neck

We describe a case of malignant glomus tumour affecting the neck of a 24-year-old woman who presented with painful neck masses and amenorrhoea. Malignant glomus tumours of the neck are rare disease and can be confused with paragangliomas. After resection surgery, postoperative complications of bilateral chylothorax (without chylous fistula) and diabetes insipidus were successfully managed, and the patient remains well after long-term follow-up.