Caso Clínico Case Report

Pulmonary lymphangioleiomyomatosis (LAM) is a rare disease of unknown aetiology. It is characterized by proliferation of abnormal smooth -muscle cells throughout the peribronchial, perivascular and perilymphatic regions of the lung. LAM may occur sporadically, in association with tuberous sclerosis complex (TSC) or inheritable multiorgan hamartomatosis 1 . In either situation, LAM occurs almost exclusively in women of reproductive age, and approximately one Linfangioleiomiomatose – A proposito de tres casos clinicos