Slowly progressive Foix-Chavany-Marie syndrome as a precursor of a primary progressive aphasia

Abstract Foix-Chavany-Marie syndrome (FCMS) is a rare neurological condition usually associated with bilateral ischemic lesions of the anterior frontoparietal operculum. Here, we present a patient with slowly progressive FCMS owing to focal brain atrophy who developed a language disorder similar to that seen in a primary progressive aphasia.