Polycystic horseshoe kidney.

Polycystic kidney disease (PKD) is a hereditary disorder of autosomal dominant or recessive inheritance. Horseshoe kidney is a common renal fusion anomaly during embryogenesis. Combination of both PKD and horseshoe kidney is rare, with an incidence of one in 1,34,000–8,00,000 live births.1 Less than twenty cases have been reported till date in adults and only one in the fetus.2,3 We report the autopsy findings of this rare anomaly in a fetus with brief review of literature.