20 In vivo monitoring of lung inflammation in CFTR–/– mice

and pulmonary disease management (ECFS; Sermet-Gaudelus et al. 2010). Results: There are currently 9 children diagnosed with CF following NBS enrolled at the paediatric CF specialized centre (14.8% of all patients), with a mean age of 11 months (range, 3–25). The mean age for confirmatory sweat test was 27 days (range, 11–48). There was a 97.1% compliance rate to ECFS guidelines (33 out of 34 recommendations), especially in the areas of nutritional and pulmonary disease management, with 100% compliance. The only area of no compliance was the lack of communication with primary care providers. Conclusions: We have identified an excellent conformity level between the care provided by the specialized CF centre and ECFS guidelines. Measures to improve communication with primary care providers are currently underway.