Dermatofibrosarcoma Protuberans (DFSP) of the Scalp with Left Neck Lymph Node Metastasis-A Case Report

Dermatofibrosarcoma protuberans (DFSP) is an unusual skin malignancy, which is locally invasive and rarely metastasizes. According to the literature, DFSP with distant metastasis is more often than regional lymph node involvement. Treatment of local DFSP is mainly surgical. A patient was noted with scalp DFSP when aged 4. Then he sustained four times of local recurrences, and left neck lymph node metastasis happened at age 19. No concurrent scalp DFSP was identified when the neck metastatic lesion was found. The previously recurred tumors were all excised, while we removed the metastatic lesion by radical neck dissection. Neither radiotherapy nor chemotherapy was done. We followed the patient for up to three years and no evidence of disease was found. DFSP with regional lymphatic metastasis is rarely seen, and literature is reviewed for the management of such patients.