Adolescent temporal bone fibrous dysplasia

Fibrous dysplasia (FD) is a rare, benign osseous tumor, whereby normal bone architecture is replaced by haphazard fibrous tissue. Temporal bone involvement is extremely rare and presents with vague symptoms. We present a case of temporal bone FD in an adolescent girl who presented with progressive unilateral hearing loss, which was successfully managed surgically with canal wall down mastoidectomy with no recurrence. FD although rare, has a tendency for cataclysmic complications if not discerned early.