ПЕРВИЧНЫЙ СКЛЕРОЗИРУЮЩИЙ ХОЛАНГИТ С ЛЕТАЛЬНЫМ ИСХОДОМ У ДЕВОЧКИ 13 ЛЕТ

Primary sclerosing cholangitis - autoimmune chronic cholestatic liver disease characterized by progressive course of latent and may proceed for many years. Naturally, the earlier the disease is detected, the longer lifespan. The article presents the clinical observation of a long asymptomatic autoimmune disease of the liver that is manifest only 6 months prior to an adverse outcome, but at the time of the manifestation of the child has already formed cirrhosis.