Juxtaglomerular cell tumor in a young male presenting with new onset congestive heart failure

Abstract Renin secreting Juxtaglomerular cell tumors are extremely rare benign tumors of the kidney. In this case, we highlight the atypical presentation of a young male patient presenting with vague complaints of worsening dyspnea, shortness of breath and anxiety. Initial workup of troponinemia and elevated BNP was initially most suggestive of a major cardiac event. An ejection fraction of 20% confirmed that this patient presented with heart failure. However, only further workup with imaging and renin and aldosterone labs revealed a functional renal mass as the cause. Timely intervention was pursued and pathology of the tumor was consistent with a juxtaglomerular cell tumor.