An unusua l presenta tion a nd a new trea tment of eccrine syringofibroadenoma

Eccrine syringofibroadenoma (ES) is a rare disease that clinically ranges from a nodule on an extremity to diffuse forms. A case of ES was assessed and compared with classification of ES. Our case had diffuse verrucous lesions since infancy, hypotrichosis, and loss of teeth. She had coincidental bullous pemphigoid. The patient was successfully treated with etretinate.