Dermatological Addendum to the 2012 International Chapel Hill Consensus Conference Nomenclature of Vasculitides

Objective The objective of this project was to prepare a dermatologic addendum to the 2012 Chapel Hill consensus conference nomenclature to address vasculitides affecting the skin. The goal was to standardize names and definitions for cutaneous vasculitis. Methods A nominal group technique with a facilitator was used to reach a consensus using multiple face-to-face meetings, e-mail discussions, and teleconferences. Results Standardized names, definitions and descriptions are provided for cutaneous components of systemic vasculitides (e.g. cutaneous IgA vasculitis as a component of systemic IgA-vasculitis), skin-limited variants of systemic vasculitides (e.g. skin-limited IgA vasculitis, drug-induced skin-limited ANCA-associated vasculitis), and cutaneous single organ vasculitides that have no systemic counterparts (e.g. nodular vasculitis). Cutaneous vasculitides that were not included in the 2012 Chapel Hill consensus conference nomenclature are introduced. Conclusions Standardized names and definitions are a prerequisite for developing validated classification and diagnostic criteria for cutaneous vasculitis. Accurate identification of specifically defined variants of systemic and skin-limited vasculitides requires knowledgeable integration of clinical, laboratory and pathology data. The proposed nomenclature for vasculitides affecting the skin provides a standard framework for both clinicians and investigators. This article is protected by copyright. All rights reserved.