Congenital Heart Deffcts in Hirschsprung’s disease: A survey in Iranian population

Congenital Heart Defects in Hirschsprung’s Disease: A Survey in Iranian Population Abstract Hirschsprung’s disease (HSCR) may be accompanied by other anomalies including congenital heart disease (CHD) resulting in additional complications. This study was performed to evaluate the prevalence and type of concomitant CHD in hospitalized children with Hirschsprung’s disease. Materials and Methods: All HSCR patients (129 children) admitted to Mofid children’s hospital-Tehran, from April 2016 to August 2019 were studied in a descriptive cross-sectional study. Two-dimensional, M-mode and pulsed, continuous, and color-Doppler provided echocardiography were applied to evaluate cardiac structure and function. Results: Congenital heart disease (CHD) was observed in 48 (37.2%) children. The most common anomalies were ASD in 20(15.5%), VSD in 1(0.8%), PDA in 2(1.6%), Tetralogy of Fallot (TF) in 3(2.3%), ASD and pulmonary stenosis (PS) in 2(1.6%), ASD and PDA in7 (5.4%), ASD and VSD in 3(2.3%), VSD and PDA in 2 (1.6%) of the patients. Conclusion: Cardiac anomalies are relatively prevalent in our Iranian Hirschsprung’s disease population. We recommend early echocardiographic evaluation in the setting of HSCR.