Complete Agenesis of the Right and Left Pulmonary Arteries, with Main Pulmonary Artery Originating from the Right Ventricle, Presenting as Primary Pulmonary Hypertension of the Newborn: Case Report

A female infant who had been misdiagnosed as having primary pulmonary hypertension of the newborn was found to have agenesis of the branch pulmonary arteries with collateral-dependent pulmonary circulation. The intracardiac anatomy was completely normal. Unifocalization of branch pulmonary artery was done, followed by stenting of the ductus arteriosus.