Ventricular Septal Myectomy for the Treatment of Left Ventricular Outflow Tract Obstruction due to Fabry Disease

Abstract Fabry cardiomyopathy can cause symptomatic left ventricular outflow tract obstruction. We review a case of Fabry cardiomyopathy mimicking hypertrophic cardiomyopathy on echocardiography with severe left ventricular outflow tract obstruction treated with ventricular septal myectomy.