Isolated Interstitial Lung Disease Associated with Anti-Ku Autoantibodies: A Case Responding to a CD20 inhibitor.

Learning Point Point 1 - This case illustrates auto-antibody testing as an essential diagnostic tool in patients with idiopathic ILD. It is the first reported case of isolated anti-Ku-related ILD without clinical manifestation of CTD. This may represent an independent pathology or a diagnosis of ILD that precedes development of clinical manifestations of a CTD.