Síndrome de Beals-Hecht: relato de um caso neonatal Beals-Hecht Syndrome: report of a neonatal case
1995
Congenital contractural arachnodactyly (CCA) is an inherited disorder of connective tissue. The most characteristic features are arachnodactyly, multiple congenital contractures, dolichostenomelia, deformed external ears, kyphoscoliosis and camptodactyly. We report a case of CCA diagnosed at birth. J. pediatr. (Rio J.). 1995; 71(6):337-340: Beals-Hecht syndrome, congenital contractural arachnodactyly, contractures.
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