Rosai-Dorfman disease in the submandibular salivary glands of a pediatric patient §

Abstract Neck mass is a common presentation in the pediatric patient. A case is discussed of a boy complaining of submandibular salivary gland enlargement, eventually leading to compressive dysphagia. Excisional biopsy yielded diagnosis of sinus histiocystosis with massive lymphadenopathy (Rosai Dorfman disease). Clinical findings, histopathology, and management of this rare disease are reviewed.