SURGICAL TREATMENT FOR A SEVERE SCOLIOSIS IN MARFAN SYNDROME BY POSTERIOR STABILIZATION

Scoliosis in Marfan syndrome is a common occurrence, constituting up to 63% prevalence. Correction is not always easy as the structural anatomy differs from the general population. We present a female 23 years old with chief complain of curved back since 10 years before admission. The patient had high stature and positive Marfan syndrome’s criteria. The patient also complained of shortness of breath. The curvature was progressive becoming more severe over time. In radiographs we found that the main thoracic curve Cobb’s angle of 920 and main lumbar curve Cobb’s angle 760. We performed scoliosis correction with pedicle screws and rod by posterior approach. Intra-operative blood loss was 1900 cc. Postoperatively, the patient had weakness at the lower limbs but resolved after several days and gained full motoric function after one week. Severe scoliosis is an indication for surgery to correct the spinal deformity that causes several complications such as pulmonary and cardiac complications. The result was satisfying proving that the procedure is safe and with proper peri-operative preparation, we may achieve a good functional outcome.