Hypertrophic pachymeningitis - Case report
2003
ABSTRACT - Hypertrophic pachymeningits is an unusual cause of neurological symptoms and is often secondaryto infections, carcinomatosis or inflammatory diseases. It may also be idiopathic. We report a case ofpachymeningitis which was manifested primarily by psychosis and visual loss with optic atrophy and destructionof nasal septum. The patient, a 45 year old woman was submitted to extensive investigation without evidenceof any underlying disease. A meningeal biopsy was performed and showed a mostly unspecific inflammatoryprocess with extensive fibrosis of the dura and few early stage granulomas. These findings suggest eitherneurosarcoidosis or idiopathic hypertrophic pachymeningitis.KEY WORDS: hypertrophic pachymeningits, neurosarcoidosis, psychosis, optic neuropathy.Paquimeningite hipertrofica: relato de casoRESUMO - Paquimeningite hipertrofica e uma causa incomum de sintomas neurologicos, sendo frequentementesecundaria a infeccoes, carcinomatose ou doencas inflamatorias. Pode tambem ser idiopatica. Relatamos umcaso de paquimeningite que se manifestou inicialmente por psicose e diminuicao da acuidade visual comatrofia optica e destruicao do septo nasal. A paciente, de 45 anos de idade, foi submetida a extensa investigacao,nao sendo evidenciada nenhuma doenca de base. Foi realizada biopsia de meninge, a qual evidenciou umprocesso inflamatorio com intensa fibrose e raros granulomas em estagio inicial. Esses achados sugeremneurossarcoidose ou paquimeningite hipertrofica idiopatica.PALAVRAS-CHAVE: paquimeningite hipertrofica, neurossarcoidose, psicose, neuropatia optica.
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