Intraosseous Neurothekeoma of the Mandible: A Rare Occurrence

Neurothekeoma, a benign dermal neoplasia, believed to be of the nerve sheath origin, is a rare condition that usually occurs in children with female predominance. It typically presents as a small, solitary, asymptomatic, subcutaneous, slow growing, and dome-shaped mass, covered by normal-looking skin. To our knowledge, this is the first reported case of an intraosseous mandibular neurothekeoma. Little is known or has been reported over the biologic behavior of this tumor when occurring in an intraosseous site. Consequently, the best treatment options and subsequent prognosis for the present case are not known. The adoption of a non-radical surgical approach in our case is supported on the premise that neurothekeoma is a benign neoplasm with a slow growth rate. The patient is presently on a monthly follow up schedule with no evidence of recurrence at one year mark. There is return of normal sensation to the patient’s right lower lip and significant regeneration of bone seen on radiographic evaluation. Of relevance is the fact that the patient has been able to resume his normal activities since very early on, participating in sports, assisting to school, and eating a regular diet.