Atrial Tachycardia in a Patient with Extracardiac Conduit Fontan Circulation

Electrophysiology (EP) studies and radiofrequency catheter ablation (RFCA) are challenging in patients who have undergone extracardiac conduit Fontan procedures, because of the difficult vascular access. Here, we report on a 14-year-old male patient who underwent extracardiac conduit Fontan procedure for a double-inlet left ventricle, complete transposition of the great arteries, and large ventricular septal defect. The EP study was performed via a trans-conduit puncture. Focal atrial tachycardia originating from the mid portion of the interatrial septum was induced. RFCA of the origin of atrial tachycardia was successfully performed. EP studies and RFCA are feasible via a trans-conduit puncture in patients with extracardiac conduit Fontan circulation.