Unusual cardiac involvement in granulomatosis with polyangiitis manifesting as acute congestive heart failure

Granulomatosis with polyangiitis (GPA), known as Wegener’s granulomatosis, is characterized by systemic necrotizing vasculitis in small and medium sized vessels affecting the upper and lower respiratory tracts, paranasal sinuses, and kidneys (1). We here describe a patient who presented with acute congestive heart failure (CHF) and progressive renal failure requiring hemodialysis and was later diagnosed with GPA based on positive renal biopsy.