Effect of Continuous Glucose Therapy (CGT) Begun in Infancy on the Long-Term Clinical Course of Patients with Type I Glycogen Storage Disease (GSD-I)† 502

We evaluated the effects of current therapy on the 24-h biochemical profile, the occurrence of significant hypoglycemia, and the long-term effects of CGT on physical growth and development, and the complications of GSD-1 in 17 patients (11 male), median age 14.2 (5.3 - 21.4) y.