Angiomatose Cutanée étendue et Phlébectasies, Avec Extrémités Acromégaloïdes. Ectasie Veineuse Rétinienne et Pharyngée Unilatérale

SummaryDescription, in a female of 50 years, of cutaneous haemangioma of right half of neck, chest and abdomen, both shoulders, upper part of back, both buttocks and, less marked, of the limbs. Marked phlebectasia of left hind limb (metameric topography) and of bend of the right arm. Aspect of veinous stasis of right eyelid, conjunctiva and fundus; also, of right hemi-pharynx.Moderate hyperplasia of right half of the body, more particularly of right arm and face. Acromegalic aspect of both hands and feet. All malformations seem congenital.Some pigmentated nœvi on the both legs (under the knees). On X-ray exami nation, bones of hands and fingers are hypertrophied but show some slight appearances of osteo-articular malformations. Hypotrophy of right cranial and facial bones. No tumor of hypophysis.Etiology and pathogenesis of case seem complex. Interference of nervous factors is proved by metameric topography of cutaneous angioma on neck, breast and abdomen, and of phlebectasia on left hind limb. Nervous pat...