Pulmoner kapak yokluğu ile birlikte olan fallot tetralojili bir olgu

Tetralogy of Fallot with absent pulmonary valve is a rare congenital heart anomaly. Pulmoner leaflets are absent and there's the aneurysmal dilatations of the tetralogy of Fallot. There's the usual malalignment ventricular septal defect, infundibular pulmonary stenosis, and overriding of the aorta. In these cases pulmonary regurgitation dominates the clinical picture. Respiratory distress is prominant due to aneurysmal dilatation. Cyanosis is slightly seen in these infants comparing with the echocardiography. Treatment is surgery. Here we report a neonate born in our hospital and diagnosed as TOF/APV in our NICU.