Respiratory distress and sudden death of a patient with GSDIb chronic neutropenia: possible role of pegfilgrastim

The advent of commercial G-CSF preparations has considerably improved the survival and quality of life of patients with chronic neutropenia,[1][1] including patients with glycogenosis Ib.[2][2] Pegylated G-CSF was authorized in the early 2000s for chemotherapy-induced neutropenia,[3][3] allowing