Mixofibrosarcoma da parede abdominal

There are few cases described of abdominal wall Myxofibrosarcoma. The authors describe the case of a 71 years old patient, who underwent urgent surgical excision of an 11 cm tumoral mass, of the internal inguinal orifice. Two months later, an excision of an 18 cm long inguinal tumor mass and multiple implants was performed. Because of a new recurrence after 4 months, a segmental bowel resection and end colostomy was performed. Patient died 6 months after first surgery. This case represents a high-grade myxofibrosarcoma, with an increasingly aggressive behavior and very short disease-free intervals, which was quickly fatal. Sarcomas are rare lesions, which initial approach should respect surgical principles and be treated by experienced teams. Keywords: Myxofibrosarcoma, high-grade, recurrence, debulking, abdominal wall.