Approach to the patients with ovotestis

Ovoteslis is a rare disorder of sexual differentiation in which the gonads have both ovarian and testicular elemenls. The patients always Present wilh ambiguous external genitalia, and there are usually with serious disorder between chromosomal sex, gonadal sex, social sex, and psychological sex. The definite diagnosis and gender coufimalion, appropriate surgery in internal genitalia and orthomorphia in external genitalia, as well as psychological support are essential for a multidisciplinary medical group in managing this disease. The medical data of two children with ovotestis who were reared as boy or girl respectively were analyzed. Key words: Disorders of sexual development ;  Ovotestis ;  Chromosomal sex ;  Gonadal sex