Isolated Form of Spongy Myocardium

Spongiform cardiomyopathy, also known as «noncompacted myocardium,» is an infrequent form of congenital cardiomyopathy resulting from a disturbance in endomyocardial embryogenesis. The diagnosis of this disease is based on typical echocardiographic findings, such as intramyocardial recesses and trabeculations. Clinical symptoms include ventricular systolic dysfunction, fundamentally of the left heart, including heart failure, ventricular arrhythmias, and embolism. Its clinical aspects and prognosis are similar to those of idiopathic dilated cardiomyopathy. We report a case of isolated spongiform cardiomyopathy with no other associated anomalies. CLINICAL CASE