Aspartylglucosaminidase

1APY, 1APZ17511593ENSG00000038002ENSMUSG00000031521P20933Q64191NM_000027NM_001171988NM_001005847NM_001205054NP_000018NP_001165459NP_001005847NP_001191983N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase is an enzyme that in humans is encoded by the AGA gene.1apy: HUMAN ASPARTYLGLUCOSAMINIDASE1apz: HUMAN ASPARTYLGLUCOSAMINIDASE COMPLEX WITH REACTION PRODUCT N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase is an enzyme that in humans is encoded by the AGA gene. Aspartylglucosaminidase is an amidohydrolase enzyme involved in the catabolism of N-linked oligosaccharides of glycoproteins. It cleaves asparagine from N-acetylglucosamines as one of the final steps in the lysosomal breakdown of glycoproteins. The lysosomal storage disease aspartylglycosaminuria is caused by a deficiency in the AGA enzyme.