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Epidermolytic hyperkeratosis

Epidermolytic ichthyosis (EI), also known as bullous epidermis ichthyosis (BEI), epidermolytic hyperkeratosis (EHK), bullous congenital ichthyosiform erythroderma (BCIE), bullous ichthyosiform erythroderma:482 or bullous congenital ichthyosiform erythroderma Brocq, is a rare and severe form of ichthyosis this skin disease affects around 1 in 300,000 people.see also Template:Congenital malformations and deformations of skin appendages, Template:Phakomatoses, Template:Pigmentation disorders, Template:DNA replication and repair-deficiency disorderAnkyrin: Long QT syndrome 4 Epidermolytic ichthyosis (EI), also known as bullous epidermis ichthyosis (BEI), epidermolytic hyperkeratosis (EHK), bullous congenital ichthyosiform erythroderma (BCIE), bullous ichthyosiform erythroderma:482 or bullous congenital ichthyosiform erythroderma Brocq, is a rare and severe form of ichthyosis this skin disease affects around 1 in 300,000 people. It involves the clumping of keratin filaments.:562

[ "Mutation", "Dyskeratosis", "Keratin", "Hyperkeratosis", "Epidermolytic acanthoma", "Generalized hyperkeratosis", "Epidermolytic Palmoplantar Keratoderma", "Bullous ichthyosis", "Keratin-2E" ]
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