The congenital lobar emphysema is a not very often found malformation. It causes during the first respirations a excessive, almost unilateral, segmental or lobar expansion. This ensues quickly a unilateral, intrathoracic high pressure with atelectasis, displacement of the mediastinum to the otherside and following extensive respiratory and circulatory derangements. The fully developed syndrom may lead to death very quickly. If diagnosis is assured, therapy of choice is to resect the involved parts of the lung.
Intrapericardial diaphragmatic hernia is characterised by a displacement of abdominal organs covered by a peritoneal diaphragm, into the pericardium. Eventration of the septum transversum can be defined morphologically but not clinically or roentgenologically. Basing on the development of the diaphragm, it would be possible to determine intrapericardial hernia as a very early inhibition malformation. - The article describes the successful outcome of treatment of a male infant, 9 months of age, who had an intrapericardial hernia.
